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Dernières publications
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Fanny Roth, Jamila Dhiab, Alexis Boulinguiez, Hadidja-Rose Mouigni, Saskia Lassche, et al.. Assessment of PABPN1 nuclear inclusions on a large cohort of patients and in a human xenograft model of oculopharyngeal muscular dystrophy. Acta Neuropathologica, 2022, ⟨10.1007/s00401-022-02503-7⟩. ⟨hal-03832636⟩
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Elisa Negroni, Maria Kondili, Laura Muraine, Mona Bensalah, Gillian Sandra Butler-Browne, et al.. Muscle fibro-adipogenic progenitors from a single-cell perspective: Focus on their “virtual” secretome. Frontiers in Cell and Developmental Biology, 2022, 10, ⟨10.3389/fcell.2022.952041⟩. ⟨hal-03830589⟩
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Ingo Riederer, Daniella Arêas Mendes-Da-Cruz, Guilherme Cordenonsi da Fonseca, Mariela Natacha González, Otavio Brustolini, et al.. Zika virus disrupts gene expression in human myoblasts and myotubes: Relationship with susceptibility to infection. PLoS Neglected Tropical Diseases, 2022, 16 (2), pp.e0010166. ⟨10.1371/journal.pntd.0010166⟩. ⟨hal-03832616⟩
Chiffres clés
98
Publications avec texte intégral
Open Access
59 %
Mots clés
Intercellular communication
Cell therapy
Myosin
BINDING SPECIFICITY
Neuromuscular junction NMJ
PABPN1 agregates
Myositis
Aged
AAV vectors
Aggregate
Cross-bridge kinetics
Autoimmune diseases
Pax7
C2C12 cells
Human
Adipose tissue
Geriatric assessment
Differentiation
ARN
Aav-U7
Dystrophie musculaire oculopharyngée
Myopathy
Skeletal muscle
Atrophy
Dystrophin
Myotube
OPMD
2-D PAGE
FSHD
DUX4
Agrégats de PABPN1
Andermann syndrome
Calcium
CS
Dysferlin
Bioinformatique
Pharyngeal muscle
Muscle strength
Alphavirus
Thérapie génique
DNA methylation
Haploinsufficiency
Inflammation
AChR antibodies
Exon-skipping
AAV
Regeneration
AUTOPHAGY
Muscle fibrosis
Alzheimer's disease
Muscle stem cells
Akt
Fibrosis
GENE
Xenograft
Myoblasts
Myogenesis
CNOT6L
Antiserum
PABPN1
Gene therapy
Functional genomics
Oculopharyngeal muscular dystrophy
Dysferlinopathy
Myoblast
Ageing
Anti-fibrotic pharmacotherapies
Bioinformatics
Transcriptomics
C2 domains
Actin
Autologous
Sarcopenia
Satellite cell
Biomarker
APOPTOSIS
Biopsies humaines
Lamins
Antisens oligonucleotides
Arbovirus
DMD
CD49d
Bile salt hydrolases
Triplet expansion disease
Satellite cells
Duchenne muscular dystrophy
Botulinum neurotoxin
MUTATIONS
Annexin A2
Muscle
Metabolism
Gene replacement
Accelerometry
RNA
ALS
Muscle dystrophy
FAPs
Anti-acetylcholine receptor antibodies
Myopathies
Nuclear envelope